Vertebral Artery Aneurysm Repair in a Vascular Ehlers-Danlos Syndrome Patient

نویسندگان

چکیده

Vertebral artery aneurysms are a rare type of vasculopathy with significant risk rupture, ischemia, and potential neurological deficits. Their location in the cervical region presents surgical challenge open endovascular options alike lack consensus on best treatment option. We present an approach to vertebral aneurysm repair patient vascular Ehlers-Danlos syndrome (type IV). A 44-year-old male was referred our health system history multifocal dissections bilateral carotid arteries. He presented complaining severe right-sided neck pain associated sharp headache. Genetic testing confirmed pathogenic variant COL3A1 gene confirming diagnosis syndrome. Computed tomography angiography revealed 1.7-cm right V1 1.4 cm left segment. Focal superior mesenteric renal arteries were also noted. recommended aneurysm. used supraclavicular access segment artery. Intravenous heparin bolus administered during phases arterial occlusion. The identified resected caudally. Reconstruction vasculature carried out creation vertebral-to-carotid bypass. Postoperative course without complications follow-up imaging widely patent carotid-to-vertebral bypass stable vessels. Our remains neurologically intact, no deficits palpable pulses. This case demonstrates Open similar cases can be good outcomes.

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ژورنال

عنوان ژورنال: Journal of Vascular Surgery

سال: 2023

ISSN: ['1085-875X', '0741-5214', '1097-6809']

DOI: https://doi.org/10.1016/j.jvs.2023.08.026